[Biventricular endomyocardiofibrosis associated with renal amyloidosis].

نویسندگان

  • José Ramos Filho
  • Carlos Alberto Fontes de Souza
  • Enzo Magrini
  • Marcelo de Macedo
  • Roberto Bauab Isolato
چکیده

Endomyocardiofibrosis is a restrictive cardiomyopathy characterized by fibrotic involvement of the endocardium and adjacent myocardium, and by diastolic dysfunction caused by changes in distensibility making ventricular filling inadequate while preserving the systolic function. Clinically, it appears as heart failure, but etiological symptomatic discernment, suspicion and a clinical examination would be necessary in order to make a correct etiological diagnosis. The case of a patient with biventricular endomyocardial fibrosis associated with renal amyloidosis is presented.

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عنوان ژورنال:
  • Arquivos brasileiros de cardiologia

دوره 85 4  شماره 

صفحات  -

تاریخ انتشار 2005